ES831000: 4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate (Disodium Salt) Pack Size:5 mg 6-Aminohexyl 2-acetamido-2-deoxy-β-D-galactopyranoside

6-Aminohexyl 2-acetamido-2-deoxy-β-D-galactopyranoside

C14H27NO11 / 385

β-GlcNAc-Et-NH2

C14H26O11S / 402

ES831000: 4-Methylumbelliferyl α-L-Idopyranosiduronic Acid 2-Sulfate (Disodium Salt) Pack Size:5 mg 6-Aminohexyl 2-acetamido-2-deoxy-β-D-galactopyranosideC16H14O12SNa2 476. 3 A 4 methylumbelliferyl glycoside of 2 O sulfated L iduronic acid (IdoA2S), supplied as the disodium salt. This is the standard fluorogenic substrate for iduronate 2 sulfatase (IDS), the lysosomal sulfatase deficient in Hunter syndrome (mucopolysaccharidosis type II), used in IDS activity assays for enzyme replacement therapy research, diagnostic screening, and inhibitor activator studies. Two sequential enzymatic reactions are